1 Matching Annotations
  1. Last 7 days
    1. 290.623 (7.5)11.1DS 3.1heterozygous VUS: c.787A>T; p.R263WNormal examinationHS 2.4heterozygous PD: c.246C>G; p.H82Q

      Case#:Patient Sample unique ID 29, Infant screened positive at birth (specimens with activity ≤15% of the DMA for enzyme activity and a CLIR screening algorithm result of indeterminate or MPS I)

      DiseaseAssertion:None

      FamilyInfo:None

      CasePresentingHPOs:None

      CaseHPOFreeText:None

      CaseNotHPOs:None

      CaseNotHPOFreeText: Normal examination at follow up after screening positive at birth (specimens with activity ≤15% of the DMA for enzyme activity and a CLIR screening algorithm result of indeterminate or MPS I)

      CaseEnzymeAssay: IDUA activity 0.623 (7.5) umol/L/h (%DMA) during new born screening through dried blood spot (plasma) and 11.1 pmol/punch/h Confirmatory IDUA enzyme

      CaseUrineGAGs: DS 3.1 g/mol creatinine and HS 2.4 g/mol creatinine (Normal)

      CaseERT:No

      CaseBMT:No

      Variant1:heterozygous VUS: c.787A>T; p.R263W (Normal examination)

      Variant1ClinVarID:2664494

      Variant1CAID:CA411263334

      Variant2: heterozygous PD: c.246C>G; p.H82Q

      Variant2ClinVarID:92637

      Variant2CAID:CA220506

      AdditionalVariants:None

      ParentalGenotype:None provided

      PreviouslyPublished:N/A